Login Contact Us
December 2014, Vol 2, Issue 5
Advanced Search
Title
Authors
Keyword
Poll
How do you find the scientific quality of the published articles on our web site?
Case Report
Ectopia Cordis and Pentalogy of Cantrell: Report of Two Cases
Murat Bakacak1, Mehmet Sühha Bostancı2, Salih Serin1, Cemil Goya3, Zeyneb Bakacak4, Fazlı Avcı1
1Kahramanmaras Sutcu Imam University, Department of Obstetrics and Gynecology, Kahramanmaras, Turkey
2Sakarya University Research and Education Hospital, Department of Obstetrics and Gynecology, Sakarya, Turkey
3Dicle University, Department of Radiology and Diagnostic Imaging, Diyarbakır, Turkey
4Specialist of Obstetrics and Gynecology, Kahramanmaras, Turkey

IJWHR 2014; 2: 323–325
DOI: 10.15296/ijwhr.2014.54
Viewed : 2325 times
Downloaded : 2934 times.

Keywords : Pentalogy of Cantrell, Ectopia Cordis, Congenital Heart Defect
Full Text(PDF) | Related Articles
Abstract
Ectopia cordis (EC) is the presence of a live, beating heart outside the thorax and is one of the most unique congenital anomalies. EC has been a weak association noted with trisomy 18 and a few cases have been associated with other chromosomal abnormalities. Pentalogy of cantrell (PC) is a rare congenital syndrome of abdominal wall defect, lower sternal defect, diaphragmatic pericardial defect, anterior diaphragmatic defect, and intracardiac abnormalities. It has a rare frequency of about 1/100,000 births. The hallmark of this syndrome is an omphalocele associated with EC. Only a few patients with the full spectrum of the pentalogy have been described. Only very few patients survive attempts at surgical repair, the main causes of death being tachyarrhythmias, bradycardia, low blood pressure, rupture of the diverticulum, and heart failure. Early diagnosis is important about discuss the option of elective termination with the parents if intracardiac anomalies of incompatible with life are noted. We report two cases of PC diagnosed in early second trimester.

Cite By, Google Scholar

Google Scholar

Articles by Bakacak M
Articles by Sühha Bostancı M
Articles by Serin S
Articles by Goya C
Articles by Bakacak Z
Articles by Avcı F

PubMed

Articles by Murat Bakacak
Articles by Salih Serin
Articles by Cemil Goya
Articles by Zeyneb Bakacak
Articles by Fazlı Avcı

Submit Paper
Online Submission System
IJWHR ENDNOTE ® Style Tutorials Publication Charge Women's Reproductive Health Research Center About Journal
Publication Information
Published Article Statistics